Anest. intenziv. Med. 2009;20(2):107-112

A fatal complication of tracheostomy in a 13-year-old patient with Duchenne Muscular Dystrophy - case reportIntesive Care Medicine - Case Report

Stříteská Jana1,*, Pařízková Renata1, Dostál Pavel1, Hoffmann Petr2, Černý Vladimír1
1 Klinika anesteziologie, resuscitace a intenzivní medicíny, UK v Praze, LF v Hradci Králové, Fakultní nemocnice Hradec Králové
2 Radiologická klinika, Fakultní nemocnice Hradec Králové

The authors describe a case of a 13-year-old boy suffering from Duchenne muscular dystrophy. Permanent mechanical ventilation was necessary due to the patient's progressive chronic respiratory insufficiency. A surgical tracheostomy was complicated by the development of tracheal stenosis managed with special types of tracheostomy tubes. A tracheo-arterial fistula developed as a result of progression of skeletal chest deformities and the tracheal stenosis. The patient died of massive arterial haemorrhage from the fistula formed between the trachea and the brachiocephalic trunk.

Keywords: Duchenne Muscular Dystrophy; tracheostomy; tracheomalacia; tracheostenosis; tracheo-arterial fistula

Received: December 15, 2008; Accepted: January 21, 2009; Published: April 1, 2009  Show citation

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Stříteská J, Pařízková R, Dostál P, Hoffmann P, Černý V. A fatal complication of tracheostomy in a 13-year-old patient with Duchenne Muscular Dystrophy - case report. Anest. intenziv. Med. 2009;20(2):107-112.
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